Gollop-Wolfgang Complex

Oumarou Habou*; Ibrahim Amadou Magagi; Harissou Adamou

Correspondence: *. Correspondence: Oumarou Habou, University of Zinder, Niger E-mail: E-mail:

Received: 2016 October 22; Accepted: 2016 October 23

J Neonat Surg. 2017 Jan 1; 6(1): 19
doi: 10.21699/jns.v6i1.492

Copyright

Copyright: © 2017 JNS



[Figure ID: F1] Figure 1: A) Left pelvic limb malformation. B) X-rays showing bifurcated fémur, tibia and patella agenesis

A full-term, 24-day-old male newborn was admitted with deformed left pelvic limb. He was born of a non-consanguineous couple without any medical history and no notion of congenital malformation in the family. The clinical examination revealed an anteromedial bony protrusion at the left knee, ipsilateral clubfoot and normal contralateral pelvic limb (Fig.1A). X-rays of the left pelvic limb showed a bifid femur with tibia agenesis and absence of the patella (Fig.1B). No further anomaly was found. Gollop-Wolfgang complex diagnosis was made.

Gollop-Wolfgang complex is a rare congenital orthopaedic malformation (1/106 live births) characterized by a distal femoral duplication and tibial agenesis associated or not with hand ectrodactyly [1,2]. The etiology of GWC is unknown and the surgical correction still difficult [1,3,4]. Excision of left sided bifurcated femur was proposed but the parents refused. Limb salvage treatment may be an alternative in this case, but would be impracticable in our context.

Footnotes

Source of Support: Nil

Conflict of Interest: None


References
1. Wada A, Nakamura T, Fujii T, Urano N, Yanagida H, Takamura K, et al. Limb salvage treatment for Gollop-Wolfgang complex (femoral bifurcation, complete tibial hemimelia, and hand ectrodactyly). J Pediatr Orthop Part B. 2013; 22:457-63.
2. Dhanakodi N, Tripathy SK. Gollop-Wolfgang syndrome. Indian J Med Res. 2014;139:963-4.
3. Endo A, Watanabe K, Shimada M, Minato M, Takada M, Takahashi S, et al. Bilateral involvement of hands and legs in the Gollop-Wolfgang complex. Am J Med Genet. 1998; 80:529–30.
4. Courvoisier A, Sailhan F, Thevenin-Lemoine C, Vialle R, Damsin JP. Congenital tibial deficiencies: treatment using the Ilizarov’s external fixator. Orthop Traumatol Surg Res. 2009; 95:431–6.

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