Duodenal atresia, annular pancreas, and situs inversus totalis- rare association in a newborn: A case report

M V LS Boris Gogan; Koto Toualouth Lafia; Codjo Serge Metchihoungbe; CA Médard Amoussou; MGI Sergine Dossou; Michel Armand Fiogbe

doi:10.47338/jns.v12.1218

Authors

M V LS Boris Gogan Department of Pediatric Surgery, National University Hospital Center, Hubert Koutoukou Maga, University of Abomey-Calavi, Benin
Koto Toualouth Lafia Department of Pediatric Surgery, National University Hospital Center “Hubert Koutoukou Maga”, University of Abomey-Calavi, Benin
Codjo Serge Metchihoungbe Department of Pediatric Surgery, National University Hospital Center “Hubert Koutoukou Maga”, University of Abomey-Calavi, Benin
CA Médard Amoussou Department of Pediatric Surgery, National University Hospital Center “Hubert Koutoukou Maga”, University of Abomey-Calavi, Benin
MGI Sergine Dossou Department of Pediatric Surgery, National University Hospital Center “Hubert Koutoukou Maga”, University of Abomey-Calavi, Benin
Michel Armand Fiogbe Department of Pediatric Surgery, National University Hospital Center “Hubert Koutoukou Maga”, University of Abomey-Calavi, Benin

DOI:

https://doi.org/10.47338/jns.v12.1218

Keywords:

Duodenal atresia, Annular pancreas, Situs inversus, Duodenojejunostomy, Neonate

Abstract

Background: Simultaneous occurrence of duodenal atresia, annular pancreas, and situs inversus totalis is an exceedingly rare clinical condition. This may pose management-related challenges to the treating surgeon.

Case Presentation: We report a case with a preoperative diagnosis of duodenal atresia and situs inversus. Intraoperatively, an annular pancreas encircling the duodenum was found. Instead of duodenoduodenostomy, a duodenojejunal anastomosis was performed. The postoperative course remained uneventful. The patient is doing fine on a 6-month follow-up.

Conclusion: The simultaneous presence of multiple anomalies in this patient prompted us to utilize an alternative approach to relieve the duodenal obstruction. This report highlights the importance of tailoring surgical decisions based on the individualized needs of the patient.

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