Duodenal atresia, annular pancreas, and situs inversus totalis- rare association in a newborn: A case report

Authors

  • M V LS Boris Gogan Department of Pediatric Surgery, National University Hospital Center, Hubert Koutoukou Maga, University of Abomey-Calavi, Benin
  • Koto Toualouth Lafia Department of Pediatric Surgery, National University Hospital Center “Hubert Koutoukou Maga”, University of Abomey-Calavi, Benin
  • Codjo Serge Metchihoungbe Department of Pediatric Surgery, National University Hospital Center “Hubert Koutoukou Maga”, University of Abomey-Calavi, Benin
  • CA Médard Amoussou Department of Pediatric Surgery, National University Hospital Center “Hubert Koutoukou Maga”, University of Abomey-Calavi, Benin
  • MGI Sergine Dossou Department of Pediatric Surgery, National University Hospital Center “Hubert Koutoukou Maga”, University of Abomey-Calavi, Benin
  • Michel Armand Fiogbe Department of Pediatric Surgery, National University Hospital Center “Hubert Koutoukou Maga”, University of Abomey-Calavi, Benin

DOI:

https://doi.org/10.47338/jns.v12.1218

Keywords:

Duodenal atresia, Annular pancreas, Situs inversus, Duodenojejunostomy, Neonate

Abstract

Background: Simultaneous occurrence of duodenal atresia, annular pancreas, and situs inversus totalis is an exceedingly rare clinical condition. This may pose management-related challenges to the treating surgeon.

Case Presentation: We report a case with a preoperative diagnosis of duodenal atresia and situs inversus. Intraoperatively, an annular pancreas encircling the duodenum was found. Instead of duodenoduodenostomy, a duodenojejunal anastomosis was performed. The postoperative course remained uneventful. The patient is doing fine on a 6-month follow-up.

Conclusion: The simultaneous presence of multiple anomalies in this patient prompted us to utilize an alternative approach to relieve the duodenal obstruction. This report highlights the importance of tailoring surgical decisions based on the individualized needs of the patient.

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References

Ruben GD, Templeton JM, Ziegler MM. Situs inversus: The complex inducing neonatal intestinal obstruction. J Pediatr Surg. 1983; 18:751-6. Available from: https://doi.org/10.1016/s0022-3468(83)80018-9.

Wabada S, Abubakar AM, Mustapha B, Pius S, Khalil J, Abana AK. Congenital duodenal obstruction due to duodenal atresia with preduodenal portal vein, annular pancreas, and intestinal malrotation associated with situs inversus abdominis: A case report. J Pediatr Surg Case Rep. 2015; 3:545-7. Available from: https://doi.org/10.1016/j.epsc.2015.10.012.

Borgaonkar VD, Deshpande SS, Kulkarni VV. Laparoscopic cholecystectomy and appendicectomy in situs inversus totalis: a case report and review of literature. J Minim Access Surg. 2011; 7:242-5. Available from: https://doi.org/10.4103/0972-9941.85649.

Al Khlaiwy O, Al Muhsin AM, Zakarneh E, Taha MY. Laparoscopic cholecystectomy in situs inversus totalis: case report with review of techniques. Int J Surg Case Rep. 2019; 59:208-12. Available from: https://doi.org/10.1016/j.ijscr.2019.05.050.

Talabi AO, Sowande OA, Tanimola AG, Adejuyigbe O. Situs inversus in association with duodenal atresia. Afr J Paediatr Surg. 2013; 10:275-8. Available from: https://doi.org/10.4103/0189-6725.120896.

Brown C, Numanoglu A, Rode H, Sidler D. Situs inversus abdominalis and duodenal atresia. a case report and review of the literature. S Afr J Surg. 2009; 47:127-30.

Nawaz A, Matta H, Hamchou M, Jacobez A, Trad O, Al Salem AH. Situs inversus abdominus in association with congenital duodenal obstruction: a report of two cases and review of literature. Pediatr Surg Int. 2005; 21:589-92. Available from: https://doi.org/10.1007/s00383-005-1412-y.

Adeyemi SD. Combination of annular pancreas and partial situs inversus: a multiple organ malrotation syndrome associated with duodenal obstruction. J Pediatr Surg. 1988; 23:188-91. Available from: https://doi.org/10.1016/s0022-3468(88)80156-8.

Iuchtman M, Golan Y, Heldenberg D, Kessler FB. Situs inversus abdominis in association with duodenal obstruction and internal hernia. Am J Perinatol. 1993; 10:255-7. Available from: https://doi.org/10.1055/s-2007-994732.

Chang J, Brueckner M, Touloukian RJ. Intestinal rotation and fixation abnormalities in heterotaxia: early detection and management. J Pediatr Surg. 1993; 28:1281-4. Available from: https://doi.org/10.1016/s0022-3468(05)80313-6.

Kayhan A, Lakadamyali H, Oommen J, Oto A. Polysplenia syndrome accompanied with situs inversus totalis and annular pancreas in an elderly patient. Clin Imaging. 2010; 34:472-5. Available from: https://doi.org/10.1016/j.clinimag.2009.11.011.

Park J, Choe BH, Chang S. Situs inversus abdominis associated with duodenal atresia: A case report. J Korean Assoc Pediatr Surg. 2009; 15:52-7. Available from: https://doi.org/10.13029/jkaps.2009.15.1.52.

Ben Ahmed Y, Ghorbel S, Chouikh T, Nouira F, Louati H, Charieg A, et al. Combination of partial situs inversus, polysplenia and annular pancreas with duodenal obstruction and intestinal malrotation. JBR-BTR. 2012; 95:257-60. Available from: https://doi.org/10.5334/jbr-btr.633.

Pattanshetti S, Peters NJ, Samujh R. Situs inversus totalis, polysplenia and annular pancreas with duodenal obstruction: A case report of bizarre embryological conundrum. Adv Pediatr Surg. 2020; 26:67-71. Available from: https://doi.org/10.13029/aps.2020.26.2.67.

Published

2023-09-05

How to Cite

1.
Gogan MVLB, Lafia KT, Metchihoungbe CS, Amoussou CM, Dossou MS, Fiogbe MA. Duodenal atresia, annular pancreas, and situs inversus totalis- rare association in a newborn: A case report. J Neonatal Surg [Internet]. 2023Sep.5 [cited 2024Feb.22];12:26. Available from: https://www.jneonatalsurg.com/ojs/index.php/jns/article/view/1218

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