Giant segmental dilatation of jejunum causing volvulus in an infant: A case report

Authors

  • Abdullah Khan The Children's Hospital & University of Child Health Sciences, Lahore
  • Assad Ameer University of Child Health Sciences, Lahore
  • Allah Ditta University of Child Health Sciences, Lahore
  • Laraib Amjad University of Child Health Sciences, Lahore
  • Kashif Nawaz University of Child Health Sciences, Lahore
  • Samina Zaman University of Child Health Sciences, Lahore
  • Nabila Talat University of Child Health Sciences, Lahore

DOI:

https://doi.org/10.47338/jns.v12.1227

Keywords:

Segmental dilatation, Jejunum, Giant, Malrotation

Abstract

Background: Giant segmental dilatation of jejunum (SDJ) is rare in small infants where it often presents with intestinal obstruction. Occasionally, the giant SDJ may twist resulting in volvulus.

Case Presentation: A 1-month-old female infant presented with intestinal obstruction. At surgery, isolated giant segmental dilatation of the jejunum causing volvulus of the bowel was found. The gut was viable. The SDJ was excised and jejuno-jejunal anastomosis was performed. Ladd’s procedure was also performed for the associated malrotation. Postoperative recovery remained uneventful.

Conclusion: Giant SDJ is a rare entity, rarer still is its presentation with volvulus secondary to its twist. Early diagnosis and prompt management result in a good outcome.

Downloads

Download data is not yet available.

Metrics

Metrics Loading ...

Author Biography

Abdullah Khan, The Children's Hospital & University of Child Health Sciences, Lahore

Resident Pediatric Surgery

References

Swenson O, Rathauser F. Segmental dilatation of the colon: a new entity. J Pediatr Surg.1959; 97:734-738.

Kasanga TK, Zeng FT, Jampy-Biaya S, Mbuyi AN, Mbuyi-Musanzayi S. Congenital segmental dilatation of the jejunum in an African child: case report. Pan Afr Med J [Internet]. 2021 [cited 2021 Aug 17];38. Available from:https://www.panafricanmedjournal.com/content/ article/38/122/full.

Mirza B, Bux N. Multiple congenital segmental dilatation of colon: a case report. J Neonatal Surg [Internet]. 2012;1:40. Available from:http://www.ncbi.nlm.nih.gov/pubmed/26023399.

Sakaguchi T, Hamada Y, Masumoto K, Taguchi T. Segmental dilatation of the intestine: results of a nationwide survey in Japan. Pediatr Surg Int. 2015; 31:1073–6.

Ben Brahim M, Belghith M, Mekki M, Jouini R, Sahnoun L, Maazoun K, et al. Segmental dilatation of the intestine. J Pediatr Surg. 2006; 41:1130‑3.

Takahashi Y, Hamada Y, Taguchi T. Segmental dilatation of the intestine. In: Taguchi T, Ed. Hirschsprung's disease and the allied disorders: status quo and future prospects of treatment, 1 sted. Singapore: Springer Nature Singapore. 2019;277-82.

Rossi R, Giacomoni MA. Segmental dilatation of the jejunum. J Pediatr Surg. 1973; 8:335-6.

Raghavan M, Arunkumar S, Balaji N. Segmental dilatation of near total colon managed by colon preserving surgery. APSP J Case Rep [Internet]. 2012 [cited 2021 Aug 18];3:18. Available from: /pmc/articles/PMC3468337/.

Ratcliffe J, Tait J, Lisle D, Leditschke JF, Bell J. Segmental dilatation of the small bowel: Report of three cases and literature review. Radiol. 1989; 171:827‑30.

Mirza MB, Maham SN, Talat N. Congenital segmental dilatation of intestine with different morphology: A case report. J Neonatal Surg. 2021; 10:41. Available from: https://doi.org/10.47338/jns.v10.1021.

Rovira J, Morales L, Parri FJ, Juliá V, Claret I. Segmental dilatation of the duodenum. J Pediatr Surg. 1989; 24:1155‑7.

Huang SF, Vacanti J, Kozakewich H. Segmental defect of the intestinal musculature of a newborn: Evidence of acquired pathogenesis. J Pediatr Surg. 1996; 31:721‑5.

Cheng W, Lui VC, Chen QM, Tam PK. Enteric nervous system, interstitial cells of Cajal, and smooth muscle vacuolization in segmental dilatation of jejunum. J Pediatr Surg. 2001;36:930‑5.

Okada T, Sasaki F, Honda S, Cho K, Matsuno Y, Itoh T, et al. Disorders of interstitial cells of Cajal in a neonate with segmental dilatation of the intestine. J Pediatr Surg. 2010; 45:e11‑4.

Adhikari SB, Rana S, Chalise S. Diagnostic dilemma of congenital segmental jejunal pseudo-dilatation associated with immature ganglion cells in the colon: A case report. J Neonatal Surg. 2020; 9:13. Available from: https://doi.org/10.47338/jns.v9.532.

Published

2023-07-21

How to Cite

1.
Khan A, Ameer A, Ditta A, Amjad L, Nawaz K, Zaman S, Talat N. Giant segmental dilatation of jejunum causing volvulus in an infant: A case report. J Neonatal Surg [Internet]. 2023Jul.21 [cited 2023Sep.25];12:21. Available from: https://www.jneonatalsurg.com/ojs/index.php/jns/article/view/1227