Rare Association of Extended Total Colonic Aganglionosis and Intestinal Malrotation

Authors

  • Iulia Stratulat-Chiriac Our Lady's Children's Hospital Crumlin
  • Danielle Mc Laughlin Our Lady's Children's Hospital Crumlin
  • Brice Antao Our Lady's Children's Hospital Crumlin

DOI:

https://doi.org/10.21699/jns.v5i4.468

Keywords:

Total colonic aganglionosis, Hirschsprung’s disease, Malrotation, Intestinal obstruction, Neonate

Abstract

Total colonic aganglionosis occurring together with malrotation is a rare occurrence and may pose diagnostic and management dilemmas for the paediatric surgeon. We report a case of a neonate that presented with extended total colonic aganglionosis and malrotation, along with a spectrum of central nervous system and renal abnormalities. The clinical and radiological features and potential diagnostic and management pitfalls are discussed along with a literature review of this exceptionally infrequent association.

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Published

2020-07-15

How to Cite

1.
Stratulat-Chiriac I, Mc Laughlin D, Antao B. Rare Association of Extended Total Colonic Aganglionosis and Intestinal Malrotation. J Neonatal Surg [Internet]. 2020Jul.15 [cited 2021Dec.2];5(4):61. Available from: https://www.jneonatalsurg.com/ojs/index.php/jns/article/view/329