Tongue shaped oropharyngeal teratoma with cleft palate in a neonate: A case report

Authors

  • Samiul Hasan Dhaka Shishu (Children) Hospital, Dhaka, Bangladesh https://orcid.org/0000-0001-5470-2241
  • Nadia Afroz National Institute of Mental Health, Dhaka, Bangladesh
  • Jiaul Reza Dhaka Shishu (Children) Hospital, Dhaka, Bangladesh

DOI:

https://doi.org/10.47338/jns.v10.929

Keywords:

Oropharyngeal teratoma, Cleft palate, Neonatal tumor, Epignathus

Abstract

Background: Atypical presentation of an atypical abnormality makes the diagnosis challenging. Oropharyngeal teratoma (epignathus) is a rare, potentially life-threatening neonatal tumor. Its atypical presentation may cause a delay in diagnosis and increase morbidity and mortality.

Case presentation: A newborn girl with oropharyngeal teratoma and cleft palate presented with feeding difficulty. The airway was patent. The tumor was tongue-shaped, smooth-walled, displacing the native tongue, and prevented the fusion of two palatine halves resulting in cleft palate. On the 4th day of life, complete excision was done transorally. Histopathology revealed a mature teratoma. There was no sign of recurrence at three months of follow-up.

Conclusion: Presentation of the oropharyngeal teratoma varies according to its site, size, and extension. Timely diagnosis is essential to avoid life-threatening respiratory obstruction. Complete excision of the mass is usually associated with a good prognosis.

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Published

2021-02-23

How to Cite

1.
Hasan S, Afroz N, Reza J. Tongue shaped oropharyngeal teratoma with cleft palate in a neonate: A case report. J Neonatal Surg [Internet]. 2021Feb.23 [cited 2021Sep.25];10:13. Available from: https://www.jneonatalsurg.com/ojs/index.php/jns/article/view/929