Vanishing gastroschisis with jejunal atresia and extreme short bowel syndrome: A case series

Authors

  • Naresh Pawar Department of Pediatric Surgery, SMS Medical College, Jaipur, Rajasthan, India.
  • Pramila Sharma Department of Pediatric Surgery, SMS Medical College, Jaipur, Rajasthan, India.
  • Punit Singh Parihar Department of Pediatric Surgery, SMS Medical College, Jaipur, Rajasthan, India.
  • Manika Boipai Department of Pediatric Surgery, SMS Medical College, Jaipur, Rajasthan, India.

DOI:

https://doi.org/10.47338/jns.v10.932

Keywords:

Vanishing gastroschisis, Extreme short bowel syndrome, Jejunal atresia

Abstract

Background: Vanishing gastroschisis may occur due to spontaneous partial or complete closure of anterior abdominal wall defect around the viscera, leading to small bowel ischemia and resultant entry/exit level atresia and extremely short length of the remaining bowel. The prognosis is very poor, even after aggressive surgery, and requires prolonged total parenteral nutrition.

Case Series: We report two female neonates, one with closed and another with closing vanishing gastroschisis, associated with jejunal atresia and extreme short bowel syndrome. In both patients, the antenatal scans showed gastroschisis without the evidence of vanishing gastroschisis. In both neonates, palliative surgeries were done. Both patients died after a few days due to short bowel syndrome and sepsis.

Conclusion: When antenatally detected gastroschisis presents with closed or closing anterior abdominal wall defect, (vanishing gastroschisis), the parents/caregivers must be counseled about the poor prognosis of this condition. A tailored approach to either palliation or aggressive therapy is essential in this rare condition.

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Author Biographies

Naresh Pawar, Department of Pediatric Surgery, SMS Medical College, Jaipur, Rajasthan, India.

Mch Resident

Pramila Sharma, Department of Pediatric Surgery, SMS Medical College, Jaipur, Rajasthan, India.

Associate Professor

Punit Singh Parihar, Department of Pediatric Surgery, SMS Medical College, Jaipur, Rajasthan, India.

Mch, Resident

Manika Boipai, Department of Pediatric Surgery, SMS Medical College, Jaipur, Rajasthan, India.

Mch, Resident

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Published

2021-01-12

How to Cite

1.
Pawar N, Sharma P, Parihar PS, Boipai M. Vanishing gastroschisis with jejunal atresia and extreme short bowel syndrome: A case series. J Neonatal Surg [Internet]. 2021Jan.12 [cited 2021Apr.13];10:7. Available from: https://www.jneonatalsurg.com/ojs/index.php/jns/article/view/932